Introduction
Gastrointestinal stromal tumors are rare soft tissue sarcomas that develop
mainly from mesenchymal tissue of gastrointestinal tract. They account for
less than 1% of all gastrointestinal tumors and originate from interstitial cells
of Cajal. Extragastrointestinal stromal tumors (E-GIST) may develop outside
gastrointestinal tract in mesentry, omentum, retroperitoneum, uterus or
vagina.
To date only, 13 cases of primary omental GISTs have been reported in
literature. Herein, we present yet another rare case of primary omental
EGIST which has been confirmed with immunohistochemical analysis
Case Report:
A 70 year old male presented with a lump in abdomen without bowel,bladder
and biliary symptoms. Patient was investigated and diagnosed as a case of
GIST with high malignant potential. At laparotomy a 23 x 18 cm size mass
arising from greater omentum was seen. Wide local excision with
omentectomy and resection of adjacent infiltrated ileal segment was done.
Postoperative course was uneventful and the patient was put on Iminitab and
is alive well with no sign of relapse at 2 years follow up.
Conclusion:
E-GIST is very rare, so it is essential to analyze accumulating data from case
reports for a better and more detailed understanding of primary omental
GISTs with regards to their clinical presentation, treatment and biological
behaviour.
Keywords: Extragastrointestinal stromal tumors, CD117, Omentum